Deep venous thrombosis (DVT) rarely occurs in conjunction with other vascular anomalies, and is therefore an understudied area. Although arteriovenous fistulae (AVF) most commonly arise from congenital defects or as a result of trauma, some reports suggest they may form in association with thrombosis of cerebral veins. In this report, we present a case of acquired pelvic and lower extremity AVFs following left common iliac vein (CIV) thrombosis. The special feature of this case is that the patient received a series of treatments of which recanalization resulted in best clinical outcome. As a result of long term follow-up (5 years), this case allows for a better understanding of the natural progression of this rare disease. Copyright © 2019 Elsevier Inc. All rights reserved.