Chordoma is a rare malignant neoplasm originating from the embryonic notochordal remnant. It is generally considered a slow-growing tumor, but it is locally aggressive and may recur after resection. Metastasis, which is more rare, may be present with the primary tumor at the time of the initial presentation, and sometimes it may occur several months or years after the diagnosis. In the present case, multiple distant metastases to the lungs, the right femur, the bilateral ilia, the left pubis, the left ischium, and the right lobe of liver were diagnosed 7 years after radical resection and radiotherapy of a sacrococcygeal chordoma. The patient and his family refused any further therapies including surgery, radiotherapy, or chemotherapy. Until now, the patient is still alive and without any significant neurological complications except sphincter disturbances.