机构:[1]Beijing Key Laboratory of Pediatric Respiratory Infectious Diseases, Key Laboratory of Major Diseases in Children, Ministry of Education, National Clinical Research Center for Respiratory Diseases, National Key Discipline of Pediatrics (Capital Medical University), Beijing Pediatric Research Institute, Beijing Children’s Hospital, Capital Medical University, National Center for Children’s Health, Beijing, China医技科室科研平台职能科室临床流行病与循证医学中心临床研究中心儿科研究所首都医科大学附属北京儿童医院
Epstein-Barr virus-positive T/NK-cell lymphoproliferative disorders (EBV + T/NK LPD) encompass a heterogeneous group of disorders, including chronic active Epstein-Barr virus infection (CAEBV), Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis (EBV-HLH), systemic EBV + T-cell lymphoma of childhood and hydroa vacciniforme-like lymphoproliferative disorder (HVLPD) and so on, predominantly affecting children and young adults with high mortality. Patients with EBV + T/NK LPD have overlapping clinical symptoms as well as histologic and immunophenotypic features. In this review, we summarized the clinical features of EBV + T/NK LPD in Chinese patients from the published articles.
基金:
Beijing Natural Science FoundationBeijing Natural Science Foundation [01-071-31]; Beijing Municipal Science & Technology CommissionBeijing Municipal Science & Technology Commission [Z181100001718061]
第一作者机构:[1]Beijing Key Laboratory of Pediatric Respiratory Infectious Diseases, Key Laboratory of Major Diseases in Children, Ministry of Education, National Clinical Research Center for Respiratory Diseases, National Key Discipline of Pediatrics (Capital Medical University), Beijing Pediatric Research Institute, Beijing Children’s Hospital, Capital Medical University, National Center for Children’s Health, Beijing, China
通讯作者:
通讯机构:[1]Beijing Key Laboratory of Pediatric Respiratory Infectious Diseases, Key Laboratory of Major Diseases in Children, Ministry of Education, National Clinical Research Center for Respiratory Diseases, National Key Discipline of Pediatrics (Capital Medical University), Beijing Pediatric Research Institute, Beijing Children’s Hospital, Capital Medical University, National Center for Children’s Health, Beijing, China
推荐引用方式(GB/T 7714):
Ai Junhong,Xie Zhengde.Epstein-Barr Virus-Positive T/NK-Cell Lymphoproliferative Diseases in Chinese Mainland[J].FRONTIERS IN PEDIATRICS.2018,6:-.doi:10.3389/fped.2018.00289.
APA:
Ai, Junhong&Xie, Zhengde.(2018).Epstein-Barr Virus-Positive T/NK-Cell Lymphoproliferative Diseases in Chinese Mainland.FRONTIERS IN PEDIATRICS,6,
MLA:
Ai, Junhong,et al."Epstein-Barr Virus-Positive T/NK-Cell Lymphoproliferative Diseases in Chinese Mainland".FRONTIERS IN PEDIATRICS 6.(2018):-